Intracranial hypertension: Think of leptomeningeal melanocytosis

Ouardia Belarbi 1; Si Ahmed Hakim2; Hatteb Samira2; Daoudi Smail2

Abstract

Intracranial hypertension: Think of leptomeningeal melanocytosis

Leptomeningeal melanocytosis is a rare primary melanocytic lesion of the central nervous system. It is considered a severe condition with poor prognosis.

It is characterized by diffuse melanocytic infiltration of the leptomeninges. Seen almost exclusively in children with large congenital nevi and together the findings form a dermatologic syndrome known as neurocutaneous melanosis (NCM).

We report a rare and atypical case of a 45-year-old adulte male, with no evident congenital melanocytic lesions who presented visual manifestations without other clinical signs of intracranial hypertension, and were found to have leptomeningeal melanocytosis with fatal evolution.

Author(s):

Ouardia Belarbi 1, Si Ahmed Hakim2, Hatteb Samira2, Daoudi Smail2

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